I-Amniotic band syndrome yimeko eyenzeka malunga nanye kwi-1,200 nganye ukuya kwi-15,000 yokuzalwa. Oku kwenza ukuba kunqabile ukuba namava, nangona kuqikelelwa ukuba kwenzeka kwi-178 kwi-10,000. Imiphumo yolu meko ingaba yanda, ihluke, kwaye idlulele kwibala ukusuka kwi-mild to severe.
Izizathu
Nangona kungekho zimpendulo ezicacileyo malunga noko kubangela i-amniotic band syndrome, inkolelo yokukhokelela kukuba ukuxilwa kokukhulelwa kwangaphambili kubangela le ngxaki.
Isikhwama se-amniotic senziwe ngamacwecwe amabini, i-amnion, kunye ne-chorion. I-amnion yinqanaba elikufutshane nomntwana wakho. Ezi zibini zombini zincinci kwaye zihambelana komnye, kodwa zisehlukene ngokwasemthethweni.
I-Amniotic band syndrome iyenzeka xa iinxalenye ze-amnion, isangqa sangaphakathi sesigxobo se-amniotic, siphula. Iimpawu ze-amniotic sac zingamathela okanye ziwele emacaleni omntwana-ezi ziyimida. Ukubambelela kungavimbela ukukhula, ukuhamba kwegazi, okanye zombini. Oku kungabangela uchungechunge oluyinkimbinkimbi lweziphene zokuzalwa, ngokuphindaphindiweyo amadijithi okanye imilenze elahlekayo, umlomo ococekileyo kunye nezinye iziphulo.
Kucatshangelwa ukuba ama-amniotic bands angenzeka ekukhulelweni kokuqala kwaye ekukhulelweni kwexesha elide ukusuka kwiziganeko ezinokuthi zikhulelwe. Xa ezi zikhefu zivela xa ukhulelwe zingenza isigqibo sokuba ubunzima buza kuba bunjani kubantwana. Ngokomzekelo, ekuqaleni, ingozi iyingozi kakhulu, kanti iqela elibonakala emva koko ekukhulelweni lingaba nantoni na.
Yintoni Amniotic Band Syndrome Ethetha Ngomntwana Wanga?
Kukho uluhlu olunzima lweengxaki ezinokuthi zihambelana nale meko. Ezinye zezi zinto zincinci, ngelixa ezinye zizinzima okanye zikwazi ukubulala. Nazi ezinye zeziphumo ezivela kulo:
- Izindandatho zokulahleka okanye ukulahlekelwa kweenxalenye zeenombolo (okanye iminwe kunye neenzwane)
- Izindandatho zokulahlekelwa okanye ukulahlekelwa kweengxenye okanye izitho zomzimba wonke (iingalo nemilenze)
- Ukuvuvukala okukhulu komzimba kwithuba elidlulileyo kwibhande
- Izandla zeClaw okanye iinyawo zeclub (ukuguquka ngokukrakra kwezandla okanye iinyawo)
- Umlomo we-Cleft kunye / okanye inhlunu (ukwahlula emlonyeni okanye kwintlungu)
- Ukukhubazeka kobuso
- Ukuguqulwa kwamanzi
- ITroracoschisis (isithintelo sodonga lwama-thoracic)
- Izidumbu zengxande
- I-Encephalocele (i-neural tube defect apho inxalenye yengqondo ixhuma ngekrele)
- I-Anencephaly (i-neural tube defect apho inxalenye yengqondo kunye neengqayi ilahlekile)
- Ukunyanzeliswa kwentambo yomlomo (ukunikezelwa kwegazi kwintambo yomzimba, ngoko ke umntwana, unqunyulwa)
- Ubunzima bodonga lomzimba (inhlanganisela yengxaki ebandakanya izitho, kunye nesifuba okanye isisu esiswini)
Iingxaki zobungqina bokukhulelwa
Nangona ukukhathazeka kwakho ngentsana yakho kukuphambili kwengqondo yakho, kukho iindaba ezilungileyo kuba oku akukho into edla ukuguqula ubude bakho bokukhulelwa. Uninzi unina alunayo ingozi eyongezelelweyo kubo okanye ukukhulelwa kwabo. Nangona kunokuba nomngcipheko omncinci wokuhambisa umntwana wakho ngaphambi kwexesha.
Omnye umba onokuthi ungabhekiswa ngokufanelekileyo uza kuba kukukhathazeka kwentlalo kunye nomoya wokuba nomntwana onenkathazo enzima njengolu.
Kwakhona, xa ukhangela ukuba akukho zininzi ezinye iintsana ezile mibuzo, ukufumana inkxaso evela kubazali abaye kwiimeko zakho akunakukulula njengoko unokuba nethemba.
Kukhona ezinye izixhobo ze-intanethi kunye namabali avela kwezinye iindwendwe eziye zenzeka kule meko, abaninzi abazimisele ukuzabelana nawe. Nangona umcimbi unokuba ungenakufumana umntu onemibandela efanayo, unikezwe uluhlu olubanzi lwamathuba. Ukuba unako ukungena kwelinye lamagumbi okubeletha okwenza utyando ukunyanga i-amniotic band syndrome, ingaba nenethiwekhi yokwesekwa engcono yokwakha.
Ukungabikho kwamanye abantu abaye bahlala kwiimeko ezifanayo, ukuthetha nabaqeqeshi abajongene nabazali kwintlekele banokukunceda. I-perinatologist yangakini okanye i-natalatal care unit iyinalo uluhlu lwemithombo, nangaphambi kokuba umntwana wakho azalwe.
Izinto zobungozi
Njengoko nayiphi na ingxaki yokukhulelwa, sihlala sijonge isizathu sokuba kwenzeke oku. Inyaniso kukuba, sisazama ukufumana isizathu esona sizathu se-amniotic band syndrome, esiyinkimbinkimbi yokujonga kwizinto ezinobungozi. Oku kuyinkimbinkimbi ngakumbi kuba kuyinqabileyo. Oko kwathiwa, sinakho iikhokelo kwizinto ezinokunyusa umngcipheko wale nkcaso engavumelekanga.
Olunye uphando lubhekisele kwinani elincinci labasetyhini kodwa lafumanisa ukuba abo babenomsebenzi wokuhlinzwa ophathelene ne-uterine babenentlungu ephezulu ye-amniotic band syndrome. Olunye uphando lubhekiselele kwimingcipheko yale nkcenkceshe emva kweempendulo ze-chorionic villus (CVS). Olu luvavanyo lokuvelisa i-genetic, apho ezinye ze-chorionic villi zisuswe ukuze zithole izimo zofuzo kumntwana. Iingcamango kukuba i-puncturing ye-sac amniotic ukwenzela ukufumana loo nto ibangela ukuba i-banding ivele. Kukho umbuzo malunga nokuba ingozi okanye ingozi enye iya kusebenza kwi- amniocentesis , eyenziwa kamva xa ukhulelwe.
Kwakukho olunye uphando oluncinane olubonise ukuba kukho ukwanda kwe-amniotic band syndrome xa umama evelele kwi-drug Misoprostol ekukhulelweni kakhulu. Oku kunikezelwa njengendlela yokukhupha isisu, kwaye akuyona iyeza eliqhelekileyo elinikezelwa kwabasetyhini abakhulelweyo.
Kukho izinto ezinobungozi ezinokuthi ziyaziwayo ngokubangela iintlobo ezininzi zeephene zokuzalwa kunye neengxaki zokukhulelwa okufuneka zinciphise okanye zisuswe xa kunokwenzeka. Oko kuquka:
- Ukutshaya xa ukhulelwe
- Ukusetyenziswa kweziyobisi ngexesha lokukhulelwa
Ndingayazi Njani Ukuba Umntwana Wami Unayo Amniotic Band Syndrome?
Amniotic band syndrome ngokuqhelekileyo ifunyenwe kwi-ultrasound, kodwa ngokuqhelekileyo ingadlulanga emva kweveki yeshumi elinesibini yokukhulelwa. Kuza kubakho iindawo ezichongiweyo nguchwepheshe we-ultrasound ukuqhubela phambili ukufunda. Oku kudla ngokubangela ukuvavanywa okongeziweyo okanye ngaphezulu kwe-ultrasound okanye mhlawumbi i-MRI. I-MRI iya kuba luncedo ekuhloleni ukuba umonakalo omkhulu wenziwe njani. Ezinye iimvavanyo ezinokuyalelwa ziquka:
- Ultrasound Targeted (3D)
- I-Doppler Blood Flow Study
- Fetal Echocardiogram
Thintelo
Okwangoku, ayikho indlela eyaziwayo ukukhusela i-amniotic band syndrome ukuba ivele. Nangona sibona ukuba ezinye iimeko zibandakanyekile ukubandakanya ukuvavanywa kwangaphambi kokubeleka, njenge-chorionic villus sampling (CVS), amanani amabhinqa akhethe ukuvavanywa okungahambiyo ahla ngokukhawuleza njengoko iimvavanyo ezincinci ezingenayo zikhoyo.
Kukho iziphakamiso eziqhelekileyo zokukhulelwa okunempilo ezingalandelwa ukuqinisekisa ukubheja kwakho ngokubhekiselele ekunciphiseni iziphene zokuzalwa. Oku kudla ngokuba yinxalenye yokunyamekela kwangaphambili.
Ziza kuba Zizinzima Kangakanani Iingxaki?
Ubunzima beengxaki ezivela kwi-amniotic band syndrome kuxhomekeka kwiimeko ezahlukeneyo. Oku kubandakanya indlela yokuqala ekukhuleleni ukuba amacandelo afakwe kwiqumrhu lomzimba okanye aphume. Ekuqaleni kokukhulelwa oku kwenzekayo, kunzima kakhulu iingxaki ziba njalo.
Unyango
Kukho iindlela ezimbini zokufumana unyango lwe-amniotic band: ngaphambi kokuba uzalwe ngophenyo lwe-fetal nangemva kokuzalwa kunye neentlobo ezahlukeneyo zokuhlinzwa kunye nezokwelapha. Kwiimeko ezininzi, i-amniotic band syndrome ayisoloko iphathwa kunyango emva kokuzalwa. Ngokuqhelekileyo, ngeli nqanaba, kunokunyamekela iimpawu kunye neyeza ukunyanga umonakalo osele usenzekile. Oku kungabandakanya unyango, ukuhlinzwa kwamathambo, ukuhlinzwa ngomlomo kunye ne-maxillofacial, okanye nokunyamekela. Ulwaphulo kunye nokuhlinzwa okusetyenziswayo kuya kuxhomekeka kwiinjongo zomzimba ezichaphazelekayo kunye nobunzima bomonakalo.
Kukho unyango olutsha olwenziwe kumaziko ambalwa eUnited States ngokusebenzisa unyango lwe-fetal ukunyanga ezinye iimeko ze-amniotic band syndrome ngexesha lokukhulelwa. Nangona akusiyo iimeko zonke ezifanelekileyo ukuhlinzwa, le ngxoxo enokufuna ukuba nayo kunye neengcali. Utyando lwe-Fetal luya kufuna ukuba uhambe kwelinye la maziko ukuze unyango kunye nokuhlinzwa. Oku kunokuthi okanye akuthethi ukuba uya kufuneka uhlale kufuphi nendawo uze uzalise.
Ukuhlinzwa okwenziwa ngumntwana, ithuluzi lepencil-size-tissed is inserted into uterus. Isetyenziselwa ukwahlula ibhendi ukukhulula ibhentshi kude nomlenze okanye inxalenye yomzimba. Ngamanye amaxesha iziphumo ziyamangalisa, omnye ugqirha uthi, ukuba ngokukhawuleza xa usebenzisa i-laser ukususa ibhola ukusuka emlenzeni womntwana, umlenze waphenduka uphindze uphindze uphindze uphindwe.
Iingxabano kunye neengozi zoPilence Surgery
Ukusetyenziswa kotyando lwe-fetal ekunakekeleni i-amniotic band syndrome akunakuphikisana. Iintlobo ezimbini eziqhelekileyo zokuhlinzwa zibandakanya ukususa ibhendi esongela intambo yomlomo, leyo, ngaphandle kokuhlinzwa, umntwana uza kufa; okanye ukususa ibhendi ukukhusela ukutsalwa kwelungu.
Ubungozi bokuhlinzwa buquka ukusuleleka, iingxaki ezivela kwi-anesthesia, ukuhanjiswa kwangethuba, kunye nezinye iingxaki. Le ingozi ingaba yingozi kwaye isetyenziswe ukuba akusiyo wonke umntu oxhasa ukuhlinzwa okwenziwa ngumntwana ukuze ulondoloze isigxina, kuba, nangona kunzima, ukuxothwa kwesilungu akuyikufa. Le miba yokuziphatha phakathi kwabazali, abasebenzi kunye neekomiti zokuziphatha zezibhedlele ezahlukeneyo.
Akukho zinto ezininzi zokuhlinzwa okanye izifundo, kodwa izifundo ezincinci ezenziweyo zibonisa izinga lokuphumelela elimalunga nama-50 ekhulwini. Oku akuveki njengempembelelo enkulu, kodwa kunikezwe ukuhlolwa kokutsalwa komntwana kunye nemingcipheko eyongeziweyo yokufuna ukuqhubeka nokukhulelwa, oku kubonwa njengepumelelo enkulu. Ithemba liwukuthi uphando oluninzi olwenziweyo, olu phezulu le nqanaba lempumelelo liya kuba. Oku kuxhomekeke ekufumaneni amacala aphezulu, kodwa nokucoca inkqubo kunye nokunyamekelwa kwenkqubo.
Ngaba Kuya kwenzeka kwakhona?
Ukuba ufumana le nto ngexesha lokukhulelwa kwakho, unokuzibuza ukuba oku kuya kuphinda kwenzeke xa ukhulelwe. Oku kubonwa njengesi-syndrome esingaphindaphindiweyo, oko kuthetha ukuba akuyi kuphinda iphinde ivele kwakhona. Nangona ngokucacileyo ukuba unako ukuphepha izinto ezinobungozi okanye ukunciphisa okanye ukunciphisa ukuba kwenzeke, unokukwazi ukuzenza uxolo lwengqondo.
Amanye amagama
Kukho amagama amaninzi amniotic band syndrome angabizwa. Ezi ziquka:
- I-syndrome yokulandelelana kwe-Amniotic
- Ibhendi yama-Amniotic
- Isondlo sesondlo sesifo
- Amacandelo eSitalat
- ADAM ulandelelwano
> Imithombo:
> Amniotic Band Syndrome. Iziko lexhala le-Fetal le-Hospital Hospital yaseWisconsin. http://www.chw.org/media-care/fetal-concerns-center/conditions/infant-complications/amniotic-band-syndrome/
> Amniotic Band Syndrome. Inhlangano kaZwelonke yeziZwe eziPhezulu (iNORD). https://rarediseases.org/rare-diseases/amniotic-band-syndrome/
> Barzilay E, Harel Y, Haas J, Berkenstadt M, Katorza E, Achiron R, Gilboa Y. Ukuxilongwa kwangaphambili kwe-amniotic band syndrome - izinto ezinobungozi kunye nezibonakaliso ze-ultrasonic. I-Matern Fetal Neonatal Med. 2015 Feb; 28 (3): 281-3. i-doi: 10.3109 / 14767058.2014.915935. Epub 2014 Meyi 22.
> Cignini, P., Giorlandino, C., Padula, F., Dugo, N., eCafà, EV, & Spata, A. (2012). I-epidemiology kunye nemingcipheko ye-amniotic band syndrome, okanye i-ADAM ngokulandelelana. Umbhalo weMithi yoPsatal , 6 (4), 59-63.
> I-Javadian P, i-Shamshirsaz AA, i-Haeri S, iRuano R, i-Ramin SM, i-Cass D, i-Olutoye i-OO, iBelfort MA. Isiphumo se-Perinatal emva kokukhululwa kwe-fetoscopic yamacandelo e-amniotic: amava aphakathi kunye nokuhlaziywa kweencwadi. Gynecol ye-Ultrasound Obstet. 2013 Oct; 42 (4): 449-55. i-doi: 10.1002 / uog.12510.